iduronate-2-sulfatase
idu·ron·ate-2-sul·fa·tase (i″du-ronґāt sulґfə-tās) [EC 3.1.6.13] a lysosomal enzyme of the hydrolase class that catalyzes the cleavage of sulfate groups from the L-iduronate residues of dermatan sulfate and heparan sulfate, a step in the degradation of these glycosaminoglycans. Deficiency of the enzyme, an X-linked recessive trait, results in Hunter syndrome (mucopolysaccharidosis II).
Medical dictionary.
2011.