- d. imperfecta [MIM*125490 & MIM*125500] an autosomal dominant disorder of the teeth characterized clinically by translucent gray to yellow-brown teeth involving both primary and permanent dentition; the enamel fractures easily, leaving exposed dentin, which undergoes rapid attrition; radiographically, the pulp chambers and canals appear obliterated and the roots are short and blunted; sometimes occurs in association with osteogenesis imperfecta; autosomal dominant inheritance. SYN: hereditary opalescent dentin (1).
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n.
the formation of dentine by odontoblast. Although dentinogenesis continues throughout life, very little dentine is formed later than a few years after tooth eruption unless it is stimulated by caries, abrasion, or trauma. Dentinogenesis imperfecta is a hereditary condition in which dentine formation is disturbed; this may result in loss of overlying enamel and excessive wear of the dentine.
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den·ti·no·gen·e·sis (den″tĭ-no-jenґə-sis) [dentin + -genesis] the formation of dentin; called also dentification.Medical dictionary. 2011.