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Gerst·mann-Sträuss·ler-Schein·ker syndrome 'gerst-mən-'s(h)trȯis-lər-'shīŋ-kər- n a rare spongiform encephalopathy that is related to Creutzfeldt-Jakob disease, is marked by ataxia, dementia, and by accumulation of amyloid plaques in the brain, and that is inherited as an autosomal dominant trait but has been transmitted experimentally to animals called also Gerstmann-Sträussler-Scheinker disease, Gerstmann-Sträussler syndrome

Scheinker I. Austrian physicians. Sträussler and Scheinker were coauthors of an article published in 1936 by Gerstmann that offered the first description of the form of encephalopathy that now bears the names of all three.

an autosomal dominant condition that resembles Creutzfeldt-Jakob disease (CJD). Patients present with cerebellar dysfunction (ataxia and dysarthria) and later develop dementia. They continue to deteriorate over several years, in contrast with patients with CJD, who deteriorate rapidly over periods of less than 12 months.